11. Anaesthesia in a patient with Prader-Willi syndrome and severe burn injury: a case report

Peter Biro

Institute of Anaesthesiology, University Hospital Zürich, CH-8091 Zürich, Switzerland

Abstract

Prader-Willi syndrome (PWS) is a congenital developmental disorder which is related to severe problems during anaesthesia. Of particular interest are the morphological and patho-physiological alterations which may lead to considerable respiratory complications, including a higher risk of regurgitation and aspiration, and the tendency towards post-surgical hypoventilation. Further difficulties may arise from mental retardation, disturbed thermoregulation, and an unstable glucose metabolism.

Keywords: Anaesthesia, co-existing disease: Prader-Willi syndrome, burns; Complications: difficult intubation, risk of aspiration, resistance to muscle relaxants.

J Rom Anest Terap Int 2011; 18: 149-152

Anestezia la un pacient cu sindrom Prader-Willi şi arsuri severe: prezentare de caz